Shamberg disease or progressive pigmented dermatosis,
chronic pigment purpura is a chronic
capillary-related disease that is located
in the skin. The disease is characterized by the appearance of pinpoints on the skin.
hemorrhages (petechiae), which tend to merge, forming extensive
conglomerates brown – brown.
It should be immediately clarified that the red color of the skin is not associated with
inflammation of the skin and has no infectious
character In this case, the pigmentation is caused by the destruction
erythrocytes and their flow through the capillaries.
Content
- Causes
- Symptoms and forms of Shamberg’s disease
- Diagnostics
- Treatment
- Prevention and prognosis
Contents
Causes
Unfortunately, the exact mechanism of the onset of Shamberg’s disease is
not identified. Many experts are inclined to believe that damage
capillary walls have an autoimmune character. In other words
the human immune system due to an unknown failure in the body,
begins to identify their own vessels as foreign. Eventually
the walls of blood vessels are damaged (broken), their
permeability, intradermal hemorrhage occurs, and part of the blood
gets under the skin. Thus, on the skin appear
notorious point hemorrhages. However, with time gems of iron,
which is found in red blood cells, turns into
pigment hemosiderin, which determines the specific color of the skin
brown brown.
Since an autoimmune disease is always a chronic process,
then the causes of Schamberg’s disease can be
triggered by the following conditions:
- Severe hypothermia and poor-quality winter clothing.
High-quality, good-quality shoes should completely close the third
shin and foot. For example, regular effects on the body
low temperatures causes cold spasm of small vessels and
violates the rheological properties of blood. As a result, damaged
vascular walls, which leads to the development of Shamberg’s disease. - A pathology such as
diabetes. The fact is that diabetes is able to run
hemosiderosis of the skin, in which destruction occurs very quickly
vascular wall. - Chronic skin disease infectious or viral
characters are able to trigger the development of Shamberg disease.
Symptoms and forms of Shamberg’s disease
Symptoms of this pathology manifest as pigment spots.
fuzzy outlines of brown – brown hue. Spots are localized
asymmetrically predominantly on the skin of the thighs, shins and
Stop. The trunk and upper limbs are affected much less frequently. On
early stages of development, small hemorrhages appear on the skin,
which tend to merge, forming a network of branched
superficial growths. The stain color is not uniform, so
along the edges of the spots new hemorrhages appear with more intense
color and vascular pattern. The disease does not cause any
subjective sensations and affects most often men.
Isomorphic reaction is characteristic of this disease (symptom
Kebner), which manifests itself in the form of fresh erythematous –
scaly eruptions in the area of skin lesions.
Shamberg disease has several forms of development that
Corresponds to the specific symptoms:
- petechial form;
- telangiectatic form;
- lichenoid form;
- eczematoid form.
The petechial form is characterized by the appearance in large
the number of spots with fuzzy edges that represent
point hemorrhages. The spots are reddish brown.
and occur predominantly in men only on the legs.
The teleangiectatic form is manifested by the appearance of spots in the form of
medallion. Spider veins are located in the center of the spot –
medallion, and at their edges are observed small red spots.
The lichenoid form is a combination of small nodules and
chiseled eruptions. Localization of spots in this form is
unconventional, that is, blemishes can form throughout the body.
The eczematoid form is a combination of point
hemorrhage and the formation of eczema. This form is the most
unpleasant because it gives the patient a certain discomfort in
itching and bubbly eruptions.
Diagnostics
The disease is diagnosed on the basis of the clinical picture. WITH
using dermatoscopy, the vascular pattern of the area is studied in detail
rash, in which there is an accumulation of fragments of capillaries and
immune cells. On the pathology of the vascular wall areas say
ulceration and necrosis, narrowing of the lumen of the capillary wall. On such
plots tend to develop thrombosis, which makes it difficult
blood flow.
The disease must be differentiated with the following
pathologies:
- purpura bateman or senile purpura;
- Purpura Mayocchi (another kind of vascular autoimmune
diseases); - varicose dermatitis;
- Kaposi’s sarcoma (with AIDS).
Treatment
The treatment strategy for treating Shamberg’s disease encompasses
three directions:
- local therapy;
- general therapy;
- bracing action.
When local therapy is used:
- ointment with corticosteroids to eliminate swelling, inflammation,
itching. - Heparin ointment to strengthen the vascular
walls.
General therapy involves the oral administration of the following
funds:
- corticosteroids;
- anti-inflammatory drugs;
- anti-sticking drugs
platelet (antiplatelet); - drugs that reduce the permeability of blood vessels and
improve microcirculation of blood.
In severe cases, techniques are shown to remove
blood factors that trigger this disease. This is the so-called
procedures for extracorporeal hemocorrection, which include
the following medical measures: cryoprecipitation, hemosorption,
plasmapheresis.
Of great importance is the observance of a hypoallergenic diet, which
excludes food allergic and irritant nature: spicy,
spicy and smoked dishes, strong tea, coffee, chocolate, citrus.
Patients with this disease should avoid hypothermia, trauma,
bruises, psycho-emotional and physical exertion. Timely
treat chronic and concomitant diseases, as
permanent foci of infection not only contribute to the development of the disease
Shamberga, but complicate and support its course.
Prevention and prognosis
Shamberg disease has a chronic course, so the prognosis
the disease is partially favorable. Complete relief of the disease
impossible, but a well-chosen treatment strategy may not
only alleviate the symptoms of the disease, but also to delay relapses.
Prevention for this disease does not exist, because before
the end does not understand the mechanisms causing it.
